Aortic atresia with interrupted aortic arch (IAA) is an exceptional condition. In
absence of associated lesion, the flow to the brain and the retrograde flow to the
coronary arteries can only come from vessels on the descending aorta. This flow needs
to be large enough to supply the brain and the myocardium. The only IAA type compatible
with survival is type C where the flow from descending aorta could be insured by the
left carotid and the left vertebral artery, branch of the left subclavian artery.
Only one such a case was described in the literature. All the other surviving cases
had an associated lesion including: a double aortic arch, an aorto-pulmonary window
(AP window), an aberrant right subclavian artery or a bilateral patent ductus arteriosus
(PDA). We report a case of aortic atresia with IAA type B associated with a double
aortic arch that underwent a successful bi-ventricular one-stage neonatal Norwood-Rastelli
repair and is doing well after 18 months.
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Article Info
Publication History
Published online: July 19, 2018
Footnotes
No funding was provided for this work.
No conflict of interest for any author.
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© 2018 Elsevier Inc. All rights reserved.
